Who has Poland syndrome? Frequency. Poland syndrome has been estimated to occur in 1 in 20,000 newborns. For unknown reasons, this disorder occurs more than twice as often in males than in females. Poland syndrome may be underdiagnosed because mild cases without hand involvement may never come to medical attention.
Frequency. Poland syndrome has been estimated to occur in 1 in 20,000 newborns. For unknown reasons, this disorder occurs more than twice as often in males than in females. Poland syndrome may be underdiagnosed because mild cases without hand involvement may never come to medical attention.
What percent of people have Poland syndrome?
Affected Populations
Estimates of its incidence have ranged from approximately one in 10,000 to one in 100,000 individuals. (Incidence refers to the number of new cases in a particular period.) As noted above, Poland Syndrome affects the right side of the body in approximately 75 percent of cases.
Is Poland’s syndrome hereditary?
Most of the time, Poland syndrome happens sporadically. This means it’s not inherited from a parent. It is more common in males than females.
People born with Poland anomaly have several physical and cosmetic disabilities, which can be treated if correctly diagnosed. Although severity and associated features vary from patient to patient, there are some common characteristics of this condition: Absence (aplasia) of some of the chest (pectoralis) muscles.
Who has Poland syndrome? – Related Questions
How serious is Poland syndrome?
In severe cases of Poland syndrome, the spine can be fused or malformed.This can lead to thoracic deformations and respiratory challenges. Certain bone defects could be present in people with Poland syndrome. This includes an underdeveloped or absent portion of ribs and cartilage where the ribs attach to the sternum.
Poland syndrome is a birth defect characterized by an underdeveloped chest muscle and short webbed fingers on one side of the body. There may also be short ribs, less fat, and breast and nipple abnormalities on the same side of the body. Typically, the right side is involved.
What can be done for Poland syndrome?
Treating Poland syndrome
Reconstructive (plastic) surgery is the most viable treatment option for Poland syndrome. It involves using existing chest wall muscles (or other muscles throughout the body as needed) to fill in missing portions. Surgery can also be used for grafting ribs to move them in the right spot.
Does Poland syndrome affect the heart?
Conclusions. These findings suggest that mechanical factors during embryonic life could explain the strong association between left-sided Poland syndrome and dextrocardia. According to this hypothesis, partial agenesis of 2 or more ribs is needed to displace the heart toward the right side.
What does Poland syndrome look like?
Disease at a Glance
Poland syndrome is characterized by an underdeveloped or absent chest muscle on one side of the body, absence of the breastbone portion (sternal) of the chest muscle, and webbing of the fingers of the hand on the same side.
How much does Poland syndrome surgery cost?
The cost of surgery for Poland syndrome varies based on your surgeon, where the surgery is being performed, and how extensive your condition is. This surgery usually costs $5,000-$10,000 but it is important to speak with Dr.
Surgical treatment of a chest wall deformity associated with Poland syndrome, including breast reconstruction, is considered medically necessary. Coverage of breast reconstruction is limited to a one- or two-stage approach to correct breast asymmetry.
How old do you have to be for Poland syndrome surgery?
Breast reconstruction in women with Poland’s syndrome with silicone implants is known and safe method. Such procedures are performed after 18 years of age.